A 50-year-old female, who had been suffered from diabetes melitus, showed typical cutaneous findinhs of dermatomyositis with only transient and mild proximal muscle weakness at sometime during the course of disease. She had Gottron's papules,
Gottron's
sign, heliotrope rasth, macular violaceous erythema invoving neck, anterior chest, back, extensor site of forearms and arms and dorsa of hands. However, her serum CPK, LDH and sGOP levels were within normal limits. Her fasting and 2hours
postprandial
blood glucose levels were elevated. There were no histological abnormality in muscle biopsy. Histopathologic findigs fo the skin lesion on her back were that of poikiloderma atrophicans vasculare.
We diagnosed our patient as Rebecca's type 2 amyopathic dermatomyositis which is chracterized by skin disease with subjective myalgias and muscle weakness, but without laboratory evidence of muscle disease. (Kor J Dermatol 1992;30 (5) :679-683)
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